报道在施行先天性外耳道闭锁手术(78耳)时发现的面神经变异和畸形、面神经水平段和/或锥体段骨管裂缺21耳;走向异常9耳,其中1耳在卵圆窗前方穿越鼓岬,5耳水平段下移,3耳垂直段向前移位;鼓室段面神经标志不清5耳.从胚胎发育角度讨论了面神经变异和畸形发生的原因及其与听骨发育的关系;结合临床讨论了面神经畸形与听力重建的关系及手术时如何预防面神经损伤. Reported facial nerve deformities and deformities, facial nerve level segments and / or septal defects in the condylar segment found during congenital external auditory canal occlusion (78 ears). The anomalous 9 ears were observed, of which 1 had traversed in front of the oval window Promontory, 5-ear horizontal section down, 3-ear vertical section forward displacement; tympanic facial nerve signs unclear 5. From the perspective of embryonic development facial nerve mutation and deformity and its relationship with the development of the ossicles; The clinical discussion of the relationship between facial nerve deformity and hearing reconstruction and how to prevent facial nerve injury during operation.