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目的 探讨肝脏血管平滑肌脂肪瘤 (HAML)这一肝脏罕见的良性肿瘤的临床特点 ,总结其治疗过程中出现的问题 ,以期提高对HAML的诊断与治疗水平。方法 通过对 5例经手术及病理证实和 1例经肝穿活检证实的HAML的诊断及治疗过程的回顾性分析 ,结合文献找出HAML所具有的共同点及特异性。结果 ①在众多的辅助检查中 ,以CT平扫及增强扫描对HAML的诊断价值最大 ;②对HAML的诊断不能仅靠单一的检查来确定 ,而要结合病史及多种化验和影像学检查来确立 ;③对HAML的手术治疗应注意操作 ,避免可能发生的并发症 ;④对症状轻微的HAML病人 ,随访观察是可行的。结论 HAML作为肝脏罕见的良性肿瘤 ,只要掌握其特征 ,做出正确的诊断与处理是完全可能的。
Objective To investigate the clinical features of hepatic angiomyolipoma (HAML), a rare benign liver tumor, and summarize the problems in the treatment process in order to improve the diagnosis and treatment of HAML. Methods A retrospective analysis of the diagnosis and treatment of HAML confirmed by surgery and pathology and confirmed by liver biopsy in 5 cases was performed. The common points and specificity of HAML were found by combining the literature. Results 1 Among the numerous auxiliary examinations, CT scan and enhanced scans were the most valuable for the diagnosis of HAML. 2 The diagnosis of HAML can not be determined by a single examination, but it should be combined with medical history and multiple laboratory and imaging examinations. Establish; 3 surgical treatment of HAML should pay attention to the operation, to avoid possible complications; 4 for patients with mild symptoms of HAML, follow-up observation is feasible. Conclusion As a rare benign tumor of the liver, HAML is entirely possible as long as its characteristics are known and correct diagnosis and treatment are made.