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[期刊论文] 作者:林青雲,陳安琪,赖志刚,陳(亻)雄,陳恩和,石志忠,湯瑞芬, 来源:中华医学杂志(英文版) 年份:2004
Mucopolysaccharidoses (MPS) are lysosomal storage diseases with defective degradation of glycosa-minoglycans. Mucopolysaccharidosis type Ⅵ (MPS Ⅵ) or Marotea...
[期刊论文] 作者:林青雲,陳安琪,赖志刚,陳偉雄,陳恩和,石志忠,湯瑞芬, 来源:Chinese Medical Journal 年份:2004
Mucopolysaccharidoses(MPS)arelysosomalstoragediseaseswithdefectivedegradationofglycosaminoglycansMucopolysaccharidosistypeⅥ(MPSⅥ)orMaroteauxLamysyndromeiscaus...
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