复习1978年至1993年House耳科诊所治疗的59例（60耳）先天性中耳胆脂瘤的手术和听力结果。讨论了其特征、手术次数和成功率。59例中，男39‘女20例，左耳33，右耳27。年龄1～59岁，平均86岁。18岁以下51例。18岁以上8例均无耳感染史，有进行性传导性耳聋，其中4例较股标志正常? Review the surgical and hearing outcomes of 59 cases (60 ears) of congenital middle ear cholesteatoma treated by the House Ophthalmic Clinic from 1978 to 1993. Discuss its characteristics, the number of operations and success rate. 59 cases, 39 males and 20 females, left ear 33, right ear 27. Ages 1-59 years old, average 86 years old. 51 under the age of 18. There was no history of ear infection in 8 cases over 18 years old, with progressive deafness, of which 4 cases were more normal than normal.