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本文叙述2例系统性红斑狼疮(SLE)合并严重再生障碍性贫血,采用羟甲雄酮(Oxymethalone)和强的松治疗后达到血液学完全缓解。当停用羟甲雄酮后均发生复发,不论有否用大剂量强的松,当用雄激素再治疗时又恢复。病例1:女性,19岁,黑人。1967年诊断为SLE。1975年4月,因癫痫大发作,开始服用二苯乙内酰脲(diphenlhydantoin)。1976年5月20日因患子宫内膜炎住进当地医院,检查白细胞1,500,中性粒细胞37%,红细胞比积18.9%,血小板51,000,网织红细胞0.8%。
This article describes two cases of systemic lupus erythematosus (SLE) complicated with severe aplastic anemia, achieved complete hematologic remission after treatment with Oxymethalone and prednisone. Recurrence occurs when dehydroepiandrosterone is discontinued, regardless of whether large doses of prednisone are used or not, and resumed when treated with androgens. Case 1: Female, 19 years old, black. 1967 diagnosed as SLE. April 1975, due to epileptic seizures, began taking diphenylhydantoin (diphenlhydantoin). May 20, 1976 due to endometritis admitted to the local hospital, check white blood cells 1,500, 37% of neutrophils, hematocrit 18.9%, 51,000 platelets, reticulocytes 0.8%.