例1:54岁,女性,患原发性自身免疫性溶贫(AIHA)已两年,间歇用皮质激素治疗。骨髓示红系明显增生。外周血Hb6.2g/dl,网织红细胞40％,白细胞及血小板正常,血片中见许多泪滴形红细胞,直接Coomb’s试验阳性,血清LDH483u/l,胆红素2.9mg/dl。查脾肋下2cm,CT检查未见腹膜后淋巴结肿大,肝脏正常,脾脏肿大。经强的松治疗两周无效行脾切除后,Hb稳定在9.3g/dl,网织红细胞15％,LDH288u/l,胆红素1.5mg/dl,脾组织切片示髓外 Example 1: 54 years old, female, suffering from primary autoimmune PTS (AIHA) for two years, intermittently treated with corticosteroids. Bone marrow showed obvious proliferation of red line. Peripheral blood Hb6.2g / dl, reticulocyte 40%, normal white blood cells and platelets, see many teardrop-shaped erythrocytes in the blood film, direct Coomb’s test positive, serum LDH483u / l, bilirubin 2.9mg / dl. Check the spleen ribs 2cm, CT no retroperitoneal lymph nodes, normal liver, enlarged spleen. After the treatment of prednisone two weeks ineffective splenectomy, Hb stable at 9.3g / dl, reticulocyte 15%, LDH288u / l, bilirubin 1.5mg / dl, spleen showed extramedullary