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McCabe 1979年首先报道了18例自身免疫性感营神经性聋(SNHL)。1984年病例数增加到56例。本文报导3例类型各异的自身免疫介导的SNHL。例1为免疫复合物介导的SNHL。患者为14岁女孩,因长期不明原因发热而就诊,主诉疲劳、不适、关节痛1年半,听力障碍6周,无耳闷、耳鸣或眩晕。检查表明双耳听力各频率对称性下降40dB,双耳重振阳性,无蜗后病变。血沉90mm,血清Ig增高,补体系统被活化,且可查见循环免疫复合物,基于心包和
McCabe first reported in 1979, 18 cases of autoimmune idiopathic neurological deafness (SNHL). In 1984 the number of cases increased to 56 cases. This article reports three different types of autoimmune-mediated SNHL. Example 1 is immune complex-mediated SNHL. The patient was a 14-year-old girl who was diagnosed with fever for unknown reasons. He complained of fatigue, malaise, joint pain for 1 and a half years, hearing impairment for 6 weeks, no ear bothersomeness, tinnitus or dizziness. Examination showed that the symmetry of the two ears decreased 40dB in each frequency, binaural vibration positive, no cochlear lesions. ESR 90mm, serum Ig increased complement system is activated, and can see circulating immune complexes, based on pericardial and