1引言间质性肺疾病是由一大组异质性疾病所组成的弥漫性、累及肺间质为主的疾病谱。分类繁多、发病机制复杂,表现缺乏特异性,诊断易致混淆。该病名称最早提出是在1975年美国第18届Aspen肺科研讨会上,之后的1985年第28届Aspen肺科研讨会上首次以间质性肺疾病为专题进行了多方面 1 INTRODUCTION Interstitial lung disease is a diffuse spectrum of diseases that predominantly involves the lungs and is composed of a large heterogeneous group of diseases. Multiple categories, complex pathogenesis, the lack of specificity of performance, diagnosis easily lead to confusion. The name of the disease was first proposed at the 18th Aspen Pulmonary Symposium in 1975 in the United States, followed by the 28th Aspen Pulmonary Symposium in 1985 for the first time in many aspects of the topic of interstitial lung disease