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组织细胞增生症X(HX)仅影响单一器官时预后良好。而多系统受累则差得多。2岁以下患儿病变累及肺、肝或骨髓者(勒-雪二氏病)病死率为50～70%。
Histopathosis X (HX) has a good prognosis when it affects only a single organ. The multi-system involvement is much worse. Patients under 2 years of age affected lung, liver or bone marrow involvement (Lehrer’s disease) mortality was 50 to 70%.